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Juvenile Huntington's Disease

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Juvenile Huntington's Disease
Huntington's disease

Anna Richards 4th period 12/7/16

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In 1872, the American physician George Huntington wrote about an illness that he called "an heirloom from generations away back in the dim past." One of its earliest names was chorea. Until recently, scientists understood very little about HD and could only watch as the disease continued to pass from generation to generation. Families saw the disease destroy their loved ones' ability to feel, think, and move. Scientist working disorders and stoke have recently got a break through with what's going on.

It is caused by getting passed down from parents. HD results from genetically programmed degeneration of nerve cells, called neurons, in certain
…show more content…
This is called Juvenile Huntington's disease. A noticeable side affect of having HD at a young age is how your rapid decline in school performance. Simple things like changes in handwriting and slight problems with movement, such as slowness, rigidity, tremor, and rapid muscular twitching, called myoclonus. One third of them have recurrent seizures. Both juvenile and adult-onset have effect of dementia.

What are the differences with juvenile and adult-onset? Both of them forms of the disease result in neurological damage that causes sever movement disorders. "But the difference is adult-onset HD is normally characterized by dance-like chorea, while juvenile HD more often results in rigidity and stiffness of muscles." Link HD Kids will most likely have the symptoms Loss of previously learned academic, physical skills, Behavioral problems, Contracted and rigid muscles that affect gait (especially in young children), bad handwriting, tremors, slight involuntary movements, or Seizures. Juvenile HD do not experience the chorea. Chorea is more likely to be present in individuals who have an age of onset from 15-18 years. Usually around age 15 they would have more adult symptoms. Juvenile onset usually results in death within 10 years. For adults usually 10-30

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